A case of ecchordosis physaliphora presenting with an intratumoral hemorrhage.
نویسندگان
چکیده
Ecchordosis physaliphora is a rare congenital, benign, hamartomatous, retroclival mass derived from notochordal tissue that is typically located intradurally in the prepontine cistern. Ecchordosis physaliphora is usually asymptomatic. In rare cases, ecchordosis physaliphora can be symptomatic due to tumor expansion and compression of the surrounding structures and extratumoral hemorrhage. To our knowledge, ecchordosis physaliphora associated with intratumoral hemorrhage and vasogenic edema has not been previously described. We present a case of 22-year-old man who presented with headache and confusion. MR imaging and CT revealed intracranial ecchordosis physaliphora associated with intratumoral hemorrhage and vasogenic edema. The neurological findings resolved completely after medical therapy.
منابع مشابه
A Unique Case Of Ecchordosis Physaliphora With Intratumoral Haemorrhage
Ecchordosis physaliphora is a small, gelatinous tissue that is considered an ectopic notochordal remnant. This tissue is located in the midline of the craniospinal axis, reaching from the dorsum sellae to the sacrococcygeal region (1-4). Intracranial EP is typically found intradurally in the pre-pontine cistern, where it is attached to the dorsal wall of clivus via a small pedicle (1, 2, 5). Ec...
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Ecchordosis physaliphora (EP) is a benign notochordal remnant derived from ectopic nests found along the craniospinal axis. It typically presents asymptomatically and is diagnosed using classic radiologic features, particularly location, T1-hypointensity, T2-hyperintensity, and lack of enhancement following gadolinium (Gd) contrast administration. Distinguishing EP from its malignant counterpar...
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عنوان ژورنال:
- Turkish neurosurgery
دوره 19 3 شماره
صفحات -
تاریخ انتشار 2009